Hendrik Biebow, b1

Diedelhof Biebout and Willemijntie Adriaens are named as parents in the record of the baptism of Hendrik Bibault on 28 May 1690 at Nederduitsch Gereformeerde Kerk, (Cape Town), de Caep de Goede Hoop.

He was thought to have been sailing on the "Zuitdorp"" for the VoC when it was wrecked on the coast of Western Australia in 1712. There was some conjecture that survivors of shipwrecks along the Western Australian coast may have introduced a mutation for variegate porphyria particularly the R59W mutation into the Aboriginal population prior to first settlement. Hendrick's parents were carriers of this disease, which had probably caused the death of 4 of their sons. Of the 296 new cases of porphyria diagnosed in Western Australia from 1978 to 1998, six had biochemically proven variegate porphyria. Three of those cases occurred in Aboriginal patients. Evidence for a possible fourth Aboriginal case of variegate porphyria is described. The R59W founder mutation responsible for over 90% of variegate porphyria in South Africa was excluded. Two new mutations that predicted amino acid substitutions with significant effects on enzyme function were detected in conserved regions of the protoporphyrinogen oxidase gene in one Aboriginal variegate porphyria patient and the possible fourth case.

CONCLUSION:

Results suggest that the mutations causing variegate porphyria in the Western Australian Aboriginal population occur sporadically and were 'not inherited' from shipwrecked sailors

NGK G1 1/1, Nederduitsch Gereformeerde Kerk, Kerken Boek (Bapt.), 1665-1695:

Den 28 Maij een kindt gedoopt waer vader is Diedelhof Biebout, en de moder Willemijntie Adriaens, ende is genaemt Hendrik beid selfs present.,

transcribed by Richard Ball, Norfolk, England, (May 2006), Genealogical Society of South Africa, eGSSA Branch http://www.eggsa.org/

Variegate Porphyrias has been traced back to 1688 when a Dutch orphan, Adriaantjie Ariens, married a Cape farmer called Gerrit Jansz van Deventer. We still do not know who carried the mutation but 4 of their 8 children inherited it, and it has become more and more common with each succeeding generation. It is widely speculated that her half-sister Wilhelmina Adriaanse de Wit Bibouw could have been a carrier. Cecilia Strauss SA mutation VP R59W

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Former President F. W. De Klerk’s autobiography The Last Trek: A New Beginning, published in 1999, begins with some intriguing revelations about the family history of the figure who presided over the dismantling of apartheid (somewhat ambivalently, it must be stated) and took on the task of leading the National Party (NP) into democracy. These revelations included that of his blood ties to an enslaved Indian woman. The author takes pains to show that “the story of the De Klerks was the story of the Afrikaner nation,” an argument he bolsters with the fact that “Hendrik Bibault, the half-brother of one of our ancestors, Susanna, was the first to call himself an Afrikaner—or an African” (De Klerk 3). The famous cry “Ik ben een Afrikaander” has often been claimed as the founding moment for “the white tribe of Africa.” De Klerk, however, takes this claim in what may be a surprising direction, given the infamous Afrikaner obsession with racial purity. Susana, he proceeds to reveal, was the daughter of a Dutch settler named Detlef Bibault and an enslaved woman named Diana of Bengal. Susana’s daughter Engela in turn married De Klerk’s “direct ancestor” Barend De Klerk in 1737 (De Klerk 4). The story of the De Klerk family and the Afrikaner nation can, in this version, only be multiracial from its very beginnings. Of course, he hastens to add: “This was part of my genealogy of which we did not speak—and of which I did not know—when I was a child” (De Klerk 4).